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KMID : 0358920090360010145
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Journal of the Korean Academy of Pedodontics
2009 Volume.36 No. 1 p.145 ~ p.149
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STURGE-WEBER SYNDROME : A CASE REPORT
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Shin Hye-Sung
Yang Kyu-Ho
Choi Nam-Ki
Kim Seon-Mi
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Abstract
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Sturge-Weber Syndrome is a rare congenital disorder and is characterized by port wine nevus following one or more divisions of trigeminal nerve, ocular involvement(eg, glaucoma) and neurologic involvement(eg, epilepsy, mental retardation). Oral menifestations include unilateral blood vessel expansion of the oral mucosa and gingiva, gingival hyperplasia, giant tooth, ipsilateral large tongue, blood vessel anomaly of maxilla or mandible and abnormal eruption sequence. This case report is about 8-year-old Sturge-Weber Syndrome patient presented violet discoloration on upper gingiva and buccal mucosa, gingival hyperplasia and abnormal eruption sequence. In this case, we performed lingual frenectomy and periodic oral hygiene management, and obtained satisfactory result.
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KEYWORD
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Sturge-Weber Syndrome, Lingual frenectomy, Port wine nevus
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